Fitzgerald/ACY1 antibody/10R-3173/100 ul
商品编号：
10R-3173-100ul
品牌：
fitzgerald-fii
市场价：
¥7900.00
美元价：
5925.00
产品分类：
功能性抗体
公司分类：
Functional_antibody
联系Q Q：
3392242852
电话号码：
4000-520-616
电子邮箱：
info@ebiomall.com
商品介绍
OVERVIEW:
| Synonyms | Monoclonal ACY1 antibody, Anti-ACY1 antibody, ACY1D antibody, ACYLASE antibody, Aminoacylase 1 antibody, ACY1, ACY 1, ACY-1, ACY 1 antibody, ACY-1 antibody |
|---|---|
| Cross Reactivity | Human, Mouse |
| Applications | FC, IHC, WB |
| Immunogen | ACY1 antibody was raised in mouse using a full length recombinant protein of human ACY1 (NP_000657) produced in HEK293 cell as the immunogen. |
SPECIFICATIONS:
| Host | Mouse |
|---|---|
| Clone | 1D4 |
| Isotype | IgG1 |
| Method of Purification | ACY1 antibody was purified by affinity chromatography. |
| Form & Buffer | Supplied in PBS buffer, pH 7.3, containing 1% BSA, 50% glycerol and 0.02% sodium azide. |
| Concentration | 500 ug-1 mg/ml |
STORAGE & SAFETY:
| Storage | Store at 4 deg C for short term storage. Aliquot and store at -20 deg C for long term storage. Avoid repeated freeze/thaw cycles. |
|---|
Usage Assay Information:
| Usage Recommendations | FC: 1:100, IHC: 1:150, WB: 1:500-2000 |
|---|
GENERAL INFORMATION:
| Biological Significance | ACY1 is a cytosolic, homodimeric, zinc-binding enzyme that catalyzes the hydrolysis of acylated L-amino acids to L-amino acids and acyl group, and has been postulated to function in the catabolism and salvage of acylated amino acids. Defects in ACY1 are the cause of aminoacylase-1 deficiency (ACY1D). ACY1D results in a metabolic disorder manifesting with encephalopathy, unspecific psychomotor delay, psychomotor delay with atrophy of the vermis and syringomyelia, marked muscular hypotonia or normal clinical features. Epileptic seizures are a frequent feature. All affected individuals exhibit markedly increased urin ary excretion of several N-acetylated amino acids. |
|---|
品牌介绍
美国Fitzgerald 公司是一家国际性知名抗体研发生产企业。Fitzgerald公司为全球试剂诊断公司与研究机构提供专业的抗体、纯化抗原以及工业诊断用大包装免疫原料。公司产品多达5000种，能够满足您对于最前沿科学研究的需求。产品涉及：单克隆抗体／抗原生育类、传染病类、TORCH系列、肿瘤标记物、心脏标记物、神经科学类、病毒类等等。
品牌分类
重组蛋白
联络我们
