菲茨杰拉德/AIPL1抗体/10R-3222/100微升
商品编号:
10R-3222-100ul
品牌:
fitzgerald-fii
市场价:
¥7900.00
美元价:
5925.00
产品分类:
功能性抗体
公司分类:
Functional_antibody
联系Q Q:
3392242852
电话号码:
4000-520-616
电子邮箱:
info@ebiomall.com
商品介绍
OVERVIEW:
Synonyms | Monoclonal AIPL1 antibody, Anti-AIPL1 antibody, Aryl hydrocarbon receptor interacting protein-like 1 antibody, LCA4 antibody, AIPL2 antibody, AIPL1, AIPL 1, AIPL-1, AIPL 1 antibody, AIPL-1 antibody |
---|---|
Cross Reactivity | Human |
Applications | FC, IF, IHC, WB |
Immunogen | AIPL1 antibody was raised in mouse using a full length recombinant protein of human AIPL1 (NP_055151) produced in HEK293T cells, as the immunogen. |
SPECIFICATIONS:
Host | Mouse |
---|---|
Clone | 3B4 |
Isotype | IgG1 |
Method of Purification | AIPL1 antibody was purified by affinity chromatography. |
Form & Buffer | Supplied in PBS buffer, pH 7.3, containing 1% BSA, 50% glycerol and 0.02% sodium azide. |
Concentration | 500 ug-1 mg/ml |
STORAGE & SAFETY:
Storage | Store at 4 deg C for short term storage. Aliquot and store at -20 deg C for long term storage. Avoid repeated freeze/thaw cycles. |
---|
Usage Assay Information:
Usage Recommendations | IF: 1:100, FC: 1:100, IHC: 1:150, WB: 1:500-2000 |
---|
GENERAL INFORMATION:
Biological Significance | Leber congenital amaurosis (LCA) accounts for at least 5% of all inherited retinal disease and is the most severe inherited retinopathy with the earliest age of onset. Individuals affected with LCA are diagnosed at birth or in the first few months of life with severely impaired vision or blindness, nystagmus and an abnormal or flat electroretinogram. The photoreceptor/pineal -expressed gene, AIPL1, encoding aryl-hydrocarbon interacting protein-like 1, was mapped within the LCA4 candidate region. The protein contains three tetratricopeptide motifs, consistent with nuclear transport or chaperone activity. AIPL1 mutations may cause approximately 20% of recessive LCA. |
---|
品牌介绍
美国Fitzgerald 公司是一家国际性知名抗体研发生产企业。Fitzgerald公司为全球试剂诊断公司与研究机构提供专业的抗体、纯化抗原以及工业诊断用大包装免疫原料。公司产品多达5000种,能够满足您对于最前沿科学研究的需求。产品涉及:单克隆抗体/抗原生育类、传染病类、TORCH系列、肿瘤标记物、心脏标记物、神经科学类、病毒类等等。
品牌分类
重组蛋白
联络我们