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当前位置: 首页 > 产品中心 > Functional_antibody > Fitzgerald/HEXA antibody/10R-8681/50 ul
商品详细Fitzgerald/HEXA antibody/10R-8681/50 ul
Fitzgerald/HEXA antibody/10R-8681/50 ul
Fitzgerald/HEXA antibody/10R-8681/50 ul
商品编号: 10R-8681-50ul
品牌: fitzgerald-fii
市场价: ¥3900.00
美元价: 2925.00
产地: 美国(厂家直采)
公司:
产品分类: 功能性抗体
公司分类: Functional_antibody
联系Q Q: 3392242852
电话号码: 4000-520-616
电子邮箱: info@ebiomall.com
商品介绍

OVERVIEW:

Synonyms Monoclonal HEXA antibody, Anti HEXA antibody, beta-hexosaminidase subunit alpha antibody, TSD antibody, hexosaminidase A antibody
Applications ELISA, WB
Immunogen HEXA antibody was raised in Mouse using recombinant human HEXA (89-529aa) purified from E. coli as the immunogen

SPECIFICATIONS:

Host Mouse
Clone AT20F1
Isotype IgG2a lambda
Method of Purification HEXA antibody was purified by protein A affinity chromatography
Form & Buffer Supplied in liquid form in Phosphate-Buffered Saline (pH 7.4) containing 10% Glycerol, 0.02% Sodium Azide
Concentration 1 mg/ml

Usage Assay Information:

Usage Recommendations ELISA: 1:3000, WB: 1:3000

GENERAL INFORMATION:

Biological Significance HEXA (Hexosaminidase A), also designated beta-Hexosaminidase A, is responsible for the degradation of GM2 gangliosides, and a variety of other molecules containing terminal N-acetyl hexosamines, in the brain and other tissues. A mutation in the a subunit of hexosaminidase is the cause of Tay-Sachs disease (TSD), also known as GM2-gangliosidosis type I. TSD is a fatal autosomal recessive lysosomal storage disease of the central nervous system (CNS) caused by insufficient activity of the HEXA enzyme that results in a failure to process GM2 gangliosides. The accumulation of GM2 ganglioside in the absence of HEXA activity causes progressive destruction of the CNS.
品牌介绍
美国Fitzgerald 公司是一家国际性知名抗体研发生产企业。Fitzgerald公司为全球试剂诊断公司与研究机构提供专业的抗体、纯化抗原以及工业诊断用大包装免疫原料。公司产品多达5000种,能够满足您对于最前沿科学研究的需求。产品涉及:单克隆抗体/抗原生育类、传染病类、TORCH系列、肿瘤标记物、心脏标记物、神经科学类、病毒类等等。